ISPR | Indian Society of Paediatric Radiology | ispr | paediatric

WHO WE ARE

The Indian Society of Paediatric Radiology (ISPR) was constituted to encourage and advance the knowledge and study of Paediatric Radiology in India since the vast knowledge of medical science needs to look at children and their medical problems in a different perspective. Diseases of children are completely different from adults including the anatomical make up of children differs from that of adults. India being the second most populous country in the world has a considerable paediatric age group population.

The society was formed so that dedicated paediatric radiologists can help, teach and promulgate the knowledge of this discipline to young and upcoming radiologists and help bridge the gap of such radiologists in our institutions which have a lack of specialized radioliogists. It is a non-profitable organization for the promotion of paediatric radiology in India and abroad to assist Government and Non-governmental agencies in all matters pertaining to paediatric radiology & medical diagnostic imaging, to encourage scientific work as well as to promote interaction among members of ISPR and allied specialists.

We hold one Mid-term National CME and one National Conference a year.
We publish an E-Newsletter twice a year for all our members.
We interact with other societies in India & in the world such as WFPI (World Federation of Paediatric Imaging) and AOSPR (Asian & Oceanic Society for Paediatric Radiology).
We have a dedicated team of office bearers with ISPR who help to carry the flag of ISPR forward.

QUIZ

JUN 2024 QUIZ
JUN QUIZ ANSWER PAGE -> LIST OF PARTICIPANTS ->
JULY 2024 QUIZ
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Fibroadipose vascular anomaly (FAVA)

FAVA usually occurs in young adults with age group between 1 and 30 years.
More common in females with male to female ratio of 1:4.
Lower extremities are more commonly involved than upper extremities. Calf muscles are most commonly involved followed by the thigh.
PIK3CA gene mutation related overgrowth spectrum disorder.

Imaging features and differential diagnoses

MRI shows well-defined or infiltrative intramuscular masses which are hyperintense on T1, T2W due to presence of fatty component. On post gadolinium sequence, low flow heterogenous enhancement is seen mainly in late arterial or venous phases. Isolated muscle involvement or transfascial extension with or without subcutaneous involvement may be seen. Dilated tortuous veins are often seen within or adjacent the mass with either normal or dilated drainage veins. Reactive bone changes may be present.
DDs - Diagnosis is often delayed and missed as it has overlapping features with other conditions like venous malformation, intramuscular hemangioma, and soft tissue tumors.
Treatment - Oral sirolimus, embolization with or without surgery. Sclerotherapy is usually ineffective.

REFERENCES

Khera PS, Garg PK, Babu S, Elhence P, Tiwari S, Nk S. Fibro Adipose Vascular Anomaly: A Rare and Often Misdiagnosed Entity. Indian J Radiol Imaging. 2021 Nov 13;31(3):776-781. doi: 10.1055/s-0041-1736399.
Erickson J, McAuliffe W, Blennerhassett L, Halbert A. Fibroadipose vascular anomaly treated with sirolimus: successful outcome in two patients.Pediatr Dermatol.2017;34(06):e317-e320.

AFFILIATES

Indian Society of Paediatric Radiology

Quiz Answer Jun 2024

Fibroadipose vascular anomaly (FAVA)

Imaging features and differential diagnoses

REFERENCES